Ammobula (sodium phenylbutyrate oral powder), 100g

Description

Product introduction

Ammobula® contains sodium phenylbutyrate, a nitrogen-scavenging medicine used in the chronic management of urea cycle disorders, a group of rare inherited metabolic disorders that impair the body’s ability to eliminate nitrogen through the normal urea cycle.

Following oral administration, sodium phenylbutyrate is converted to phenylacetate, which combines with glutamine to form phenylacetylglutamine. This compound is subsequently eliminated through the urine, providing an alternative pathway for nitrogen removal and helping reduce the risk of excessive ammonia accumulation.

Ammobula® is used under the supervision of a physician experienced in the management of urea cycle disorders and is generally used together with appropriate dietary and nutritional management.

Product Introduction

Ammobula® is a specialized rare-disease medicine intended for patients with urea cycle disorders who require nitrogen-scavenging therapy. Treatment and dosing should be individualized according to the patient’s age, body weight or body surface area, clinical condition, and specialist medical advice.

Uses of Ammobula®

• Used as adjunctive therapy for the long-term management of urea cycle disorders.
• Helps manage elevated ammonia levels associated with impaired urea-cycle function.
• Used in patients with specific urea-cycle enzyme deficiencies, as prescribed by a specialist.
• May be used in both pediatric and adult patients when clinically appropriate.

Benefits of Ammobula® in Treatment

• Provides an alternative pathway for nitrogen disposal.
• Helps reduce the accumulation of excess ammonia.
• Supports long-term metabolic management of urea cycle disorders.
• Can be incorporated into a comprehensive treatment plan involving dietary and nutritional management.
• Available as an oral powder formulation for administration according to prescribed dosing instructions.

Side Effects of Ammobula®

Possible side effects may include:

• Nausea and vomiting
• Decreased appetite
• Abdominal discomfort or pain
• Headache
• Altered or unpleasant taste
• Body odor
• Menstrual irregularities in some patients

Patients should contact their healthcare professional if they experience persistent, severe, or unusual symptoms.

Quick Tips

• Take Ammobula® exactly as prescribed by your healthcare professional.
• Do not change the dose or stop treatment without medical advice.
• The prescribed dose is generally divided throughout the day with meals or feeds.
• The powder may be mixed with appropriate food or liquid as directed.
• Maintain the recommended dietary and nutritional plan.
• Regular monitoring of ammonia and other relevant laboratory parameters may be required.
• Store the product as directed and keep the container tightly closed.
• Urea cycle disorders require specialist management; seek urgent medical attention for symptoms suggestive of a hyperammonemic crisis.

To Order

oder@srkpharma.com